Asymmetrical nevus flammeus

Last Updated: 2019-08-26

Author(s): Anzengruber, Navarini

Lateral nevus, flammeus nevus, portwine stain, vinosus nevus.

Congenital or early-stage malformation of capillaries and postcapillary venules located laterally of the midline.

There has been no vascular innervation, which reduces the vascular tone, resulting in vasodilatation.

  • Red wine coloured, purple, sharply defined maculae. The reddening disappears due to the compression of the glass spatula pressure.
  • Associated malformations 
    • Pphacomatosis pigmentovascularis
    • Congenital Angiodysplasia Syndromes

In the case of periorbital localization, an ophthalmological examination (glaucoma, retinal damage) is indicated.

Subepidermal capillary dilatation.

  • Laser therapy (argon laser, 532 nm Nd:YAG laser)
  • Do not take any surgical measures!
  1. Senti G, Trueb RM. [Acquired naevus flammeus (Fegeler syndrome)]. Vasa 2000;29:225-8.
  2. Achtelik W, Tronnier M, Wolff HH. [Combined naevus flammeus and naevus fuscocoeruleus: phacomatosis pigmentovascularis type IIa]. Hautarzt 1997;48:653-6.
  3. Taute BM, Podhaisky H, Wiegand E, Eifert S, Behrmann C. [Unilateral giant extremity growth, naevus flammeus and chronic venous insufficiency in a 48-year-old patient]. Internist (Berl) 1998;39:308-11.
  4. Johnson SC, Hanke CW. Unilateral acquired nevus flammeus in women. Cutis 2001;67:225-8.