Hydroa vacciniformia
Last Updated: 2019-08-27
ICD11: -
Last Updated: 2019-08-27
Author(s): Anzengruber F., Navarini A.
ICD11: -
Bazin 1862
Rare photodermatosis.
Mostly occurring in early childhood.
Frequency peak: spring.
Unknown.
Possibly associated with the Ebstein-Bar virus.
Erythema, papules, urticaria and blisters. In contrast to the polymorphic light reaction, scarring also occurs after blister formation. Central necrosis can also occur.
Anamnesis
Clinical picture
Biopsy
Direct immunofluorescence
Photoprovocation (UVA)
Porphyrins in stool and serum (e.g. porphyria)
Areas exposed to light.
Intra- and subepidermal acantholysis. Possibly necroses.
UV protection.
Light-hardening.
In acute stage: Elocom Crème 1x day.
Spontaneous relief of symptoms in young adulthood.
Di Lernia V, Mansouri Y. Epstein-Barr virus and skin manifestations in childhood. Int J Dermatol. 2013 Oct;52(10):1177-84.