Keratosis palmplantaris papulosa Buschke-Fischer-Brauer

Last Updated: 2023-07-07

Author(s): Anzengruber F., Navarini A.

ICD11: EC20.32

Buschke and Fischer 1910

Brewer 1913

Palmoplantar keratosis, which is associated with an increased risk  of malignancy.

A autosomal – dominant inheritance is assumed, although the mutated gene is not known.

Mostly in/after puberty, various symptoms appear for the first time.

Punctate hyperkeratosis palmoplantar.

Nail dystrophies.

Increased risk of lymphoma and solid tumours.



Tumour – Search

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  3. Podder I, Das A, Bhattacharya S, Shome K, Chowdhury SN. Buschke-Fischer-Brauer Keratoderma: Linear Variety Associated with Hodgkin's Lymphoma. Indian J Dermatol. 2015 May-Jun;60(3):322.