Monilethrix
Last Updated: 2019-08-27
ICD11: -
Last Updated: 2019-08-27
Author(s): Anzengruber F., Navarini A.
ICD11: -
Smith 1879
Aplasia pilorum moniliformis, Aplasia pilorum intermittens, Aplasia moniliformis, spindle hairs, pearled hairs
Hereditary hair growth disorder with increased fragility.
Usually inconspicuous hair at birth. In the first months of life, fragile, brittle hair with regular tufts (knots) occurs. In some cases, the hair can break off very close to the hair root, leading to "pseudoalopecia".
Possible associations:
Trichogram (regular distensions (nodi) are pathognomic).
In a few cases, hair grows again in the course of life.
No treatment possible.