Neurofibromatosis 1
Last Updated: 2021-11-19
ICD11: LD2D.10
Last Updated: 2021-11-19
Author(s): Anzengruber F., Navarini A.
ICD11: LD2D.10
From Recklinghausen 1882
Peripheral neurofibromatosis, neurofibromatosis generalisata, Recklinghausen's disease, NF, NF-1.
Autosomal-dominantly inherited neuroectodermal systemic disease.
≥2 criteria must be met for a diagnosis:
Surgical excision of tumours