Overview of skin lymphomas WHO-EORTC classification (2018)

Mycosis fungoides, Sézary syndrome (SS), Adult T-cell leukemia/lymphoma (HTLV+), Primary cutaneous CD30+ lymphoproliferative disorders, Primary cutaneous anaplastic large cell lymphoma (PCALCL), Lymphomatoid papulosis (LyP), Subcutaneous panniculitis-like T-cell lymphoma (SPTCL), Extranodal NK/T-cell lymphoma, Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma (provisional), Cutaneous γ/δ T-cell lymphoma (provisional), Primary cutaneous small-medium pleomorphic T-cell lymphoma (provisional), Primary cutaneous follicular B-cell lymphoma (PCFCL), Primary cutaneous marginal zone B-cell lymphoma (PCMZL), Primary cutaneous diffuse large B-cell lymphoma, Primary cutaneous intravascular large B-cell lymphoma.

Current WHO-EORTC classification (2018)

• Cutaneous T cell lymphoma:
  • Mycosis fungoides (MF)
  • MF variants
    • Folliculotropic MF
    • Pagetoid reticulosis
    • Granulmatous slack skin
    • Sezary Syndrome
    • Adult T Cell leukemia / lymphoma
  • Prinary cutaneous CD30+ LPDs
    • C-ALCL
    • Lymphomatoid papulosis
    • Subcutaneous panniculitis-like T cell lymphoma
    • Extranodal NK/T cell lymphoma, nasal type
    • Chronic active EBV infection
  • Primary cutaneous T cell lymphoma, rare subtypes
    • Primary cutaneous gamma/delta T cell lymphoma
    • CD8+ AECTCL (provisional)
    • Primary cutaneous CD4+ small/medium T cell lymphoproliferative disorder (provisional)
    • Primary cutaneous acral CD8+ T cell lymphoma (provisional)
    • Primary cutaneous peripheral T cell lymphoma, NOS
• Cutaneous B cell lymphoma:
  • PCMZL
  • PCFCL
  • PCDLBLC, LT
  • EBV+ mucocutaneous ulcer (provisional)
  • Intravascular large B cell lymphoma