Hydroa vacciniformia

Last Updated: 2023-07-07

Author(s): Anzengruber F., Navarini A.

ICD11: EJ30.Y

Bazin 1862

  • Hidroa vacciniforme
  • Hidroa vacciniformis
  • Hidroa vacciniformia

Rare photodermatosis.

Mostly occurring in early childhood.

Peak of incidence: spring.

Unknown.

Possible association with Epstein-Bar virus.

Erythema, papules, urticaria and blisters. Unlike the polymorphous light reaction, scarring also occurs after blister formation. Central necrosis may also occur.

Anamnesis

Clinical picture

Biopsy

Direct immunofluorescence

Photoprovocation (UVA)

Porphyrins in stool and serum (e.g. porphyria)

Light-exposed areas.

Intra- and subepidermal acantholysis. Possibly necrosis.

UV protection.

Light-hardening.

In the acute stage: Elocom cream 1x tgl.

 

Spontaneous resolution of symptoms in young adulthood.

 

  1. Nitiyarom R, Wongpraparut C. Hydroa vacciniforme and solar urticaria. Dermatol Clin. 2014 Jul;32(3):345-53

  2. Di Lernia V, Mansouri Y. Epstein-Barr virus and skin manifestations in childhood. Int J Dermatol. 2013 Oct;52(10):1177-84.

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