Primär kutanes intravaskuläres grosszelliges B-Zell-Lymphom

Zuletzt aktualisiert: 2021-06-27

Autor(en): Anzengruber

ICD11: 2A81.1

Pfleger und Tappeiner 1959.

Angioendotheliomatosis proliferans systemitisata.

Seltenes B-Zell-Lymphom.

  • Männer = Frauen
  • Häufigkeitsgipfel: ≥ 60. J

Aufgrund intravaskulärer Tumorzellinfiltrate kommt es zu einer Okklusion kleinerer Gefässe.

  • Im Bereich der Beine und des Unterbauchs zeigen sich wenig charakteristische rötliche, infiltrierte, teils leicht bläuliche, teils ulzerierte Knoten und Plaques.
  • ↓ AZ, Fieber, B-Symptomatik, neurologische Ausfallserscheinungen (Demzenz, Seh- und Sprachstörungen).
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