Übersicht der Hautlymphome WHO-EORTC Klassifikation (2018)

Synonyme

Mycosis fungoides, Sézary Syndrom (SS), Adulte T-Zell Leukemie/Lymphom (HTLV+), Primär kutane CD30+ lymphoproliferative Erkrankungen, Primär kutanes anaplastisches großzelliges Lymphom (PCALCL), Lymphomatoide Papulose (LyP), Subkutanes Pannikulitis-artiges T-Zell-Lymphom (SPTCL), Extranodales NK/T-Zell-Lymphom, Primär kutanes aggressives epidermotropes CD8+ T-Zell-Lymphom (provisorisch), Kutanes γ/δ T-Zell-Lymphom (provisorisch), Primär kutanes klein-mittelgroßzelliges pleomorphes T-Zell-Lymphom (provisorisch), Primär kutanes follikuläres B-Zell-Lymphom (PCFCL), Primär kutanes Marginalzonen B-Zell-Lymphom (PCMZL), Primär kutanes diffus-großzelliges B-Zell- Lymphom, Primär kutanes intravaskuläres großzelliges B-Zell-Lymphom.

Einteilung

Current WHO-EORTC classification (2018)

Cutaneous T cell lymphoma:
- Mycosis fungoides (MF)
- MF variants
  - Folliculotropic MF
  - Pagetoid reticulosis
  - Granulmatous slack skin
  - Sezary Syndrome
  - Adult T Cell leukemia / lymphoma
- Prinary cutaneous CD30+ LPDs
  - C-ALCL
  - Lymphomatoid papulosis
  - Subcutaneous panniculitis-like T cell lymphoma
  - Extranodal NK/T cell lymphoma, nasal type
  - Chronic active EBV infection
- Primary cutaneous T cell lymphoma, rare subtypes
  - Primary cutaneous gamma/delta T cell lymphoma
  - CD8+ AECTCL (provisional)
  - Primary cutaneous CD4+ small/medium T cell lymphoproliferative disorder (provisional)
  - Primary cutaneous acral CD8+ T cell lymphoma (provisional)
  - Primary cutaneous peripheral T cell lymphoma, NOS
Cutaneous B cell lymphoma:
- PCMZL
- PCFCL
- PCDLBLC, LT
- EBV+ mucocutanous ulcer (provisional)
- Intravascular large B cell lymphoma

Referenzen

Willemze et al. The 2018 update of the WHO-EORTC classification of primary cutaneous lymphomas, Blood 2018. https://doi.org/10.1182/blood-2018-11-881268