Blastic neoplasia of plasmacytoid dendritic cells
Last Updated: 2023-07-07
Author(s): Anzengruber F., Navarini A.
Aggressive neoplasia, which primarily starts on the skin and becomes generalised leukaemic in the course of the disease.
- Peak in frequency: 70-80 y
- Exanthematous, reddish-brown, asymptomatic plaques and nodules on the trunk and head
- Involvement of CNS and bone marrow is typical
The average survival time is 12-14 months.
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